Subject(s)
Humans , Female , Adult , Pulmonary Subvalvular Stenosis/complications , Echocardiography/methods , Endocarditis/complications , Echocardiography, Doppler/methods , Ultrasonography/methods , Hypertrophy, Right Ventricular , Heart Atria , Heart Defects, Congenital/complications , Heart Defects, Congenital/diagnosis , Heart Septal Defects, Atrial , Heart VentriclesABSTRACT
Aneurysm of the main pulmonary artery is rare. Its natural history is not well understood and there are no clear guidelines regarding its optimal treatment. We present a case of a huge saccular aneurysm of the main pulmonary artery which was associated with infundibular and valvular pulmonary stenosis. It was repaired using a pericardial patch with concomitant pulmonary valvotomy and infundibular resection. Postoperative recovery was uneventful and the patient is doing well. Follow-up echocardiogram revealed good repair.
Subject(s)
Aneurysm/complications , Cardiovascular Surgical Procedures , Humans , Male , Middle Aged , Pulmonary Artery/pathology , Pulmonary Subvalvular Stenosis/complications , Ventricular Outflow Obstruction/complicationsABSTRACT
The cardiac manifestation usually associated with tuberous sclerosis is rhabdomyoma of the heart. We report a rare association with cyanotic congenital heart disease in the form of double outlet right ventricle with infundibular pulmonary stenosis.
Subject(s)
Child , Double Outlet Right Ventricle/complications , Female , Humans , Pulmonary Subvalvular Stenosis/complications , Tuberous Sclerosis/complicationsABSTRACT
Fifty one angiographically proved cases of tetralogy of Fallot (TOF) in the age group of 5-50 years were analysed retrospectively for the level(s) of right ventricular outflow tract (RVOT) obstruction. Mean age was 18.1 +/- 11 yrs. Subvalvular stenosis was found to be the commonest site of RVOT obstruction in 49 (96.1%) patients. Evidence of valvular pulmonary stenosis was seen quite commonly (42/51, 83.9% cases), mostly in association with obstruction at other sites. Supravalvular stenosis was also seen in 17 (33.3%) cases. Higher incidence of pulmonary valvular involvement in patients with TOF, in higher average age of patient population may represent valvular involvement to be an acquired phenomenon.